Arrhythmogenic right ventricular cardiomyopathy

Fast Beats

Overview

What will you do when your best friend’s heart skips a beat while dancing the night away? Will you end his dreams of running a marathon?


  1. Diagnosis of arrhythmogenic right ventricular cardiomyopathy (ARVC)
  2. Exercise and ARVC
  3. Issues with ICDs
  4. Which treatment option?
  1. ACC/AHA/ESC 2006 Guidelines for Management of Patients With Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death: A Report of the American College of Cardiology/American Heart Association Task Force and the European Society of Cardiology Committee for Practice Guidelines (Writing Committee to Develop Guidelines for Management of Patients With Ventricular Arrhythmias and the Prevention of Sudden Cardiac Death): Developed in Collaboration With the European Heart Rhythm Association and the Heart Rhythm Society. Circulation [online]. 2006;114:e385-e484; originally published online August 25, 2006 [viewed 28th April 2014]; doi: 10.1161/CIRCULATIONAHA.106.178233
  2. ACC/AHA/HRS 2008 Guidelines for Device-Based Therapy of Cardiac Rhythm Abnormalities: A Report of the American College of Cardiology/American Heart Association Task Force on Practice Guidelines (Writing Committee to Revise the ACC/AHA/NASPE 2002 Guideline Update for Implantation of Cardiac Pacemakers and Antiarrhythmia Devices): Developed in Collaboration With the American Association for Thoracic Surgery and Society of Thoracic Surgeons. Circulation [online]. 2008;117:e350-e408 [viewed 28th April 2014]; originally published online May 15, 2008; doi: 10.1161/CIRCUALTIONAHA.108.189742
  3. CORRADO D, LEONI L, LINK MS, BELLA PD, et al. Implantable Cardioverter-Defibrillator Therapy for Prevention of Sudden Death in Patients With Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia. Clinical Investigation and Reports. Circulation [online].2003; 108: 3084-3091[viewed 28th April 2014] doi: 10.1161/ 01.CIR.0000103130.33451.D2
  4. GEMAYEL C, PELLICCIA A, THOMPSON PD. Arrhythmogenic right ventricular cardiomyopathy. J Am Coll Cardiol [Online]. 2001;38(7):1773-1781[viewed 28th April 2014]. doi:10.1016/S0735-1097(01)01654-0
  5. MARCUS FI, MCKENNA WJ,SHERRIL D, BASSO C,et al.Diagnosis of Arrhythmogenic Right Ventricular Cardiomyopathy/ Dysplasia. Proposed modification of the task force criteria. Circulation [Online].2010; 121: 1533-1541 [viewed 28th April 2014] Available from doi: 10.1161/ CIRCULATIONAHA.108.840827
  6. MARON BJ, ACKERMAN MJ, NISHIMURA RA, PYERITZ RE,et al. Task Force 4: HCM and other cardiomyopathies, mitral valve prolapse, myocarditis, and Marfan syndrome. Am Coll Cardiol [online]. 2005;45(8):1340-1345 [viewed 28th April 2014]. doi:10.1016/j.jacc.2005.02.011
  7. MCKENNA WJ, THIENE G, NAVA A, FONTALIRAN F,et al. Diagnosis of arrhythmogenic right ventricular dysplasia/ cardiomyopathy. Br Heart J [online]1994;71:215-218 [viewed 28th April 2014] Available from http://heart.bmj.com/content/71/3/215.long
  8. NAVA A, BAUCE B, BASSO C, MURIAGO M, et al. Clinical profile and long-term follow-up of 37 families with arrhythmogenic right ventricular cardiomyopathy. J Am Coll Cardiol [online]. 2000;36(7):2226-2233 [viewed 28th April 2014]. doi:10.1016/S0735-1097(00)00997-9